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双肺移植治疗儿童囊性纤维化的多学科综合诊疗

王胜飞 陈静瑜 刘懿 郑明峰 毛文君

王胜飞, 陈静瑜, 刘懿, 等. 双肺移植治疗儿童囊性纤维化的多学科综合诊疗[J]. 器官移植, 2021, 12(2): 184-190. doi: 10.3969/j.issn.1674-7445.2021.02.008
引用本文: 王胜飞, 陈静瑜, 刘懿, 等. 双肺移植治疗儿童囊性纤维化的多学科综合诊疗[J]. 器官移植, 2021, 12(2): 184-190. doi: 10.3969/j.issn.1674-7445.2021.02.008
Wang Shengfei, Chen Jingyu, Liu Yi, et al. Multi-disciplinary team of the treatment of bilateral lung transplantation for pediatric cystic fibrosis[J]. ORGAN TRANSPLANTATION, 2021, 12(2): 184-190. doi: 10.3969/j.issn.1674-7445.2021.02.008
Citation: Wang Shengfei, Chen Jingyu, Liu Yi, et al. Multi-disciplinary team of the treatment of bilateral lung transplantation for pediatric cystic fibrosis[J]. ORGAN TRANSPLANTATION, 2021, 12(2): 184-190. doi: 10.3969/j.issn.1674-7445.2021.02.008

双肺移植治疗儿童囊性纤维化的多学科综合诊疗

doi: 10.3969/j.issn.1674-7445.2021.02.008
基金项目: 

江苏省科教强卫工程青年医学重点人才项目 QNRC2016193

详细信息
    作者简介:

    王胜飞,男,1995年生,硕士研究生,研究方向为肺移植及体外膜肺氧合,Email:ianwang0710@163.com

    通讯作者:

    郑明峰,男,1968年生,主任医师,研究方向为肺移植,Email:zhengmfmedical@126.com

    毛文君,男,1987年生,副主任医师,研究方向为肺移植,Email:maowenjun1@126.com

  • 中图分类号: R61, R622

Multi-disciplinary team of the treatment of bilateral lung transplantation for pediatric cystic fibrosis

More Information
  • 摘要:   目的  通过多学科综合诊疗(MDT)模式提高双肺移植治疗儿童囊性纤维化的外科疗效。  方法  对1例国内罕见的终末期囊性纤维化10岁患儿进行肺移植术前MDT讨论,制定对应治疗方案。  结果  患儿确诊囊性纤维化5年,肺移植指征明确,经过MDT讨论决定行Clam-shell切口下双肺移植术,术中维持生命体征稳定,术后给予呼吸机辅助通气、抗感染、免疫抑制、抑酸和预防应激性溃疡等治疗,并根据患儿特点给予个体化治疗方案,术后恢复良好。  结论  通过肺移植术前MDT讨论,肺移植治疗儿童囊性纤维化的手术效果满意,减少了术后并发症的发生风险,值得临床推广。
  • 图  1  肺囊性纤维化患儿围手术期胸部影像学表现和支气管镜探查表现

    注:A图示患儿术前胸部CT检查图像;B图示患儿术后第4日胸部CT检查图像;C图示患儿出院前胸部CT检查图像;D图示患儿术后3个月复查胸部CT检查图像;E图示患儿术后第1日X线胸片检查图像;F图示患儿术后第6日X线胸片检查图像;G图示患儿术前纤维支气管镜探查图像;H图示患儿术后第1日床边纤维支气管镜探查图像。

    Figure  1.  The perioperative chest imaging findings and bronchoscopy findings in the child with pulmonary cystic fibrosis

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出版历程
  • 收稿日期:  2020-12-26
  • 网络出版日期:  2021-03-19
  • 刊出日期:  2021-03-15

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